Bariatric Surgery in a Patient with Factor VII Deficiency: A Case Report

Authors

  • Arbaab Khan MD, Post-Doctoral Researcher, Department of General Surgery, Saudi-German Hospital
  • Abdulaziz AlJuhaini General and Obesity Surgery Consultant, Saudi German Hospital

DOI:

https://doi.org/10.51699/ijhsms.v2i1.987

Keywords:

Factor VII Deficiency, Bariatric Surgery, Sleeve Gastrectomy, Coagulopathy

Abstract

Bariatric Surgery in patients with congenital bleeding disorders is a challenge requiring an integrated approach of various departments. Inherited factor VII deficiency is the most common of the rare bleeding disorders, with a wide range of haemorrhagic features. Although bariatric surgery is a common procedure of the 21st century, it is seldom practised in individuals with congenital haemorrhagic disorders. Here, we highlight the course of a patient with coagulation factor VII deficiency who underwent successful bariatric surgery without significant coagulopathy. Perioperative bleeding in the patient’s case was successfully prevented by administration of 2 units of Fresh frozen Plasma.

Downloads

Download data is not yet available.

References

Lapecorella M, Mariani G, International Registry on Congenital Factor VII Deficiency. Factor VII deficiency: defining the clinical picture and optimizing therapeutic options. Haemophilia. 2008;14(6):1170-1175.

Mariani G, Konkle BA, Ingerslev J. Congenital factor VII deficiency: therapy with recombinant activated factor VII -- a critical appraisal. Haemophilia. 2006;12(1):19-27.

Benlakhal F, Mura T, Schved J, Giansily-Blaizot M; French Study Group of Factor VII Deficiency. A retrospective analysis of 157 surgical procedures performed without replacement therapy in 83 unrelated factor VII-deficient patients. J Thromb Haemost. 2011;9(6):1149-1156.

Giansily-Blaizot M, Verdier R, Biron-Adréani C, et al. Analysis of biological phenotypes from 42 patients with inherited factor VII deficiency: Can biological tests predict the bleeding risk? Haematologica. 2004;89(6):704-709.

Mariani G, Dolce A, Batorova A, et al. Recombinant, activated factor VII for surgery in factor VII deficiency: A prospective evaluation - the surgical STER. Br J Haematol. 2011;152(3):340-346.

Napolitano M, Di Minno M, Batorova A, Mariani G. Women with congenital factor VII deficiency: Clinical phenotype and treatment options from two international studies. Haemophilia. 2016;22(5):752-759.

Downloads

Published

2023-02-01

How to Cite

Khan, A. ., & AlJuhaini, A. . (2023). Bariatric Surgery in a Patient with Factor VII Deficiency: A Case Report . INTERNATIONAL JOURNAL OF HEALTH SYSTEMS AND MEDICAL SCIENCES, 2(1), 93–95. https://doi.org/10.51699/ijhsms.v2i1.987

Issue

Section

Articles